首页> 外文期刊>Respiration: International Review of Thoracic Diseases >Bronchiolitis obliterans organizing pneumonia: a distinct pulmonary complication in cystic fibrosis (see comments)
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Bronchiolitis obliterans organizing pneumonia: a distinct pulmonary complication in cystic fibrosis (see comments)

机译:闭塞性细支气管炎组织性肺炎:囊性纤维化的明显肺部并发症(请参阅评论)

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摘要

Organizing pneumonia in cystic fibrosis has hitherto been considered a nonspecific reparative process. We report on an adult patient with cystic fibrosis and histologically proven bronchiolitis obliterans organizing pneumonia, who experienced sustained clinical improvement under corticosteroid therapy. This case suggests that bronchiolitis obliterans organizing pneumonia may be a distinct pulmonary complication in cystic fibrosis and improve with specific therapy. Copyright 2000 S. Karger AG, Basel.
机译:迄今为止,在囊性纤维化中组织性肺炎被认为是非特异性的修复过程。我们报道了一名患有囊性纤维化和组织学证实的闭塞性细支气管炎组织性肺炎的成年患者,该患者在糖皮质激素治疗下经历了持续的临床改善。这种情况表明,组织性肺炎闭塞性细支气管炎可能是囊性纤维化的一种独特的肺部并发症,并通过特定的治疗得以改善。版权所有2000 S. Karger AG,巴塞尔。

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