RELAXING RETINECTOMY FOR TRACTIONAL RETINAL DETACHMENT WITH RETINAL CAPILLARY HEMANGIOMAS IN GENOTYPICALLY CONFIRMED von HIPPEL-LINDAU DISEASE

摘要

Purpose: To report the outcome of tractional retinal detachment with retinal capillary hemangiomas after pars plana vitrectomy (PPV) and relaxing retinectomy in genotypically confirmed von Hippel-Lindau disease (VHL).Methods: Interventional case report of a 28-year-old patient with multiple and large retinal capillary hemangiomas underwent PPV combined with relaxing retinectomy.Results: Over the next several weeks, the retina recovered to reattachment and remained this way for 2 years. In excised angiomas, the finding of a missense Arg167Trp mutation and immunohistochemistry staining confirmed the diagnosis of VHL.Conclusion: Patients with tractional retinal detachment with hemangiomas secondary to VHL may benefit from PPV with relaxing retinectomy.