Proteus Takayasu's arteritis with unusual intracranial granulomatosis as initial manifestation

摘要

Takayasu's arteritis (TA) is an inXammatory vasculitis of aorta and its branches, its low incidence limited our recognition to this entity. We sometimes can confuse this desease with polyarteritis nodosa and other vasculitis when no conventional "big artery" involved in TA cases. Here we report a 26-year-old man with Takayasu's arteritis who presented with a provisional intracranial granulomatosis Wrst and then saccular aneurysms between celiac trunk and arteria hepatica communis and many other proteus manifestations, which is seldom described before.