Langerhans cell histiocytosis of the clivus: An unusual cause of a destructive central skull base mass in a child

摘要

A 25-year-old man presented with a history of occipital headache of 6 weeks duration and a single seizure 4 weeks before admission. He had no neurologic deficit or neurocutaneous markers. Computed tomography (CT) of brain revealed a cystic lesion with a mural nodule in the right parieto-occipital lobe [Figure la and b]. Magnetic resonance imaging (MRI) showed a well-defined cystic lesion (5.7 x 3.4cm) with a solid mural nodule lateral to the occipital horn of right lateral ventricle. [Figure lc andd]. The provisional diagnosis was pilocytic astrocytoma or pleomorphic xanthoastrocytoma. He underwent right parieto-occipital craniotomy and excision of the tumor through transcortical trans-sulcal approach.