Clinical and Pathological Findings of a Fatal Sys Capillary Leak Syndrome (Clarkson Disease) A Case Report

摘要

Systemic capillary leak syndrome (SCLS) is a rare disorder with episodes of hypotension, hypoalbuminemia, and hemoconcentration. During attacks endothelial hyperpermeability results in leakage of plasma proteins into the interstitial space. Attacks vary in severity and may be lethal.