A rare case of cerebral vasculitis in Henoch-Schonlein purpura with emphasis on the diagnostic value of magnetic resonance angiography (MRA) and single-photon emission computed tomography (SPECT) given normal magnetic resonance imaging (MRI).

摘要

Henoch-Schonlein purpura (HSP) is a small-vessel vasculitis that is the most common cause of non-thrombocytopenic purpura in children. The classic manifestations are palpable purpura, arthralgia, abdominal pain, and glomerulone-phritis. Although the nervous system is less commonly involved, neurological symptoms and signs occur in a significant proportion of HSP cases. Several cases of cerebral vasculitis in HSP have been reported. To identify the presence and extent of cerebral vasculitis, MRI and magnetic resonance angiography (MRA) have been used as crucial diagnostic tools. In this article, we report a case of cerebral vasculitis in an HSP patient using a new modality, ~(99m)Tc-hexamethylpropyleneamine oxime (HMPAO) single-photon emission computed tomography (SPECT) with acet-azolamide, in addition to MRI and MRA.