The Vitreo-Retinal Manifestations of Persistent Hyperplasic Primary Vitreous (PHPV) and Their Management

摘要

Persistent hyperplastic primary vitreous (PHPV) has been called by various names, such as persistent tunica vasculosa lentis, persistent posterior fetal fibrovascular sheath of the lens, congenital retinal septum, and ablation falciformis congential. It was first reported by Jules Cloquet in 1818 in Memoire sur la membrane pupillae, et sur la formation du petit cercle arteriel de l'iris. In 1949, Reese defined this entity histopathologically. In 1955, Reese coined the term persistent hyperplastic primary vitreous (PHPV) a congenital anomaly in which the embryonic hyaloid vasculature fails to regress normally. In 1997, Goldberg renamed this entity as persistent fetal vasculature (PFV) as to encompass the complete spectrum of the disease.