Dejerine-Sottas disease (progressive hypertrophic polyneuropathy).

摘要

This paper records parts of Dejerine and Sottas's description of the syndrome that bears their names. It outlines biographical elements of Dejerine's work. The modern classification and the role of myelin protein mutations are briefly described. Neurology and art , Dejerine-Sottas disease , Hereditary motor and sensory neuropathy , Myelin proteins