We described a male infant with a spectrum of anomalies compatible with the diagnosis of lsquo;diorganization-like syndromersquo;. The infant had a partial foot arising form the right buttock, an absent right kidney, and a shortened right leg with severe non-positional talipes equinovarus. The infant's karyotype was 47,XXY. The right common iliac artery was one half of the expected diameter. The limb reduction defect seen in this case disorganization (Ds) may have had a vascular aetiology
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