AbstractWe present electrodiagnostic data on 30 patients with inclusion body myosistis (IBM) in order to better delineate its electrophysiological features. Comprehensive electromyography (EMG) and nerve conduction studies (NCS) were performed in all cases. Twelve patients had single fiber electromyography (SFEMG). EMG showed abundant short‐small motor unit potentials (MUP) with fibrillations and positive sharp waves in 56.6 of patients, and a mixed pattern of large and small MUP in 36.7. In 6.7, only “neurogenic” features were seen. NCS were slow in 33.3. SFEMG revealed a mildly abnormal jitter and a slightly increased fiber density. IBM demonstrates a heterogeneous EMG profile. A pattern of large and small MUP is highly suggestive of IBM but is seen in only about one third of
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机译:摘要我们介绍了30例包涵体肌骨炎(IBM)患者的电诊断数据,以更好地描述其电生理特征。所有病例均进行了全面的肌电图 (EMG) 和神经传导研究 (NCS)。12例患者行单纤维肌电图(SFEMG)。56.6%的患者肌电图显示丰富的短小运动单位电位(short-small motor unit potential, MUP),伴有纤维性颤动和正尖波,36.7%的患者出现大小MUP混合模式。在6.7%中,仅观察到“神经源性”特征。NCS在33.3%中表现缓慢。SFEMG显示轻微异常抖动和纤维密度略有增加。IBM 演示了异构 EMG 配置文件。大 MUP 和小 MUP 的模式高度暗示 IBM,但仅在大约 1/3 的
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