机译：Cutaneous barrier leakage and gut inflammation drive skin disease in Omenn syndrome
Univ Milan, Dept Food Environm & Nutr Sci, Milan, Italy;
NCI, Lab Pathol, Ctr Canc Res, NIH, Bethesda, MD 20892 USA;
NIAID, Lab Clin Immunol & Microbiol, Natl Inst Hlth NIH, Bethesda, MD 20892 USANatl Res Council CNR, Milan Unit, Inst Genet & Biomed Res IRGB, Via Manzoni 113, I-20089 MilanHumanitas Clin & Res Ctr IRCCS, Milan, ItalyUniv Milano Bicocca, Ctr Ric Tettamanti, Clin Pediat, Monza, ItalyKuwait Univ, Fac Med, Dept Pediat, Kuwait, KuwaitUniv Autonoma Estado Morelos, Fac Med, Cuernavaca, Morelos, MexicoTech Univ Dresden, Dept Pediat, Med Fak Carl Gustav Carus, Dresden, GermanyGreat North Childrens Hosp, Clin Resource Bldg, Newcastle Upon Tyne, Tyne & Wear, EnglandNHGRI, NIH, Bethesda, MD 20892 USAUniv Brescia, Dept Mol & Translat Med, Brescia, ItalyAmer Univ, Dept Pediat & Adolescent Med, Beirut Med Ctr, Beirut, LebanonHarvard Med Sch, Div Immunol, Boston Childrens Hosp, Boston, MA 02115 USAUniv Ziekenhuis Leuven, Univ Hosp Leuven, Dept Pediat, Leuven, BelgiumKatholieke Univ Leuven, Dept Imaging & Pathol, Lab Translat Cell & Tissue Res, Leuven, BelgiumParis Descartes Sorbonne Paris Cite Univ, Imagine Inst, Paris, FranceUniv Med Ctr Ulm, Dept Pediat & Adolescent Med, Ulm, GermanyChildrens Hosp Bambino Gesu, Dept Pediat, Rome, ItalyLeidos Biomed Res Inc, Frederick Natl Lab Canc Res, Neutrophil Monitoring Lab, Frederick, MD USANIAID, Fungal Pathogenesis Sect, Lab Clin Immunol & Microbiol, Bethesda, MD 20892 USA;
RAG; T cells; skin inflammation; erythroderma; immune-mediated disease; cytokines; chemokines; gut-skin axis; LPS; dysbiosis;
