Hanging Undifferentiated Embryonal Sarcoma of the Liver in Adult: an Unusual Presentation of an Aggressive Tumor

摘要

Introduction: Undifferentiated embryonal sarcoma of the liver (UESL) is a rare, highly aggressive hepatic neoplasm of mesenchymal origin seen almost exclusively in pediatric population. It was termed UESL for the first time by Stocker et al. in 1978 [2]. This disease is very rare in adults with less than 70 cases reported in English literature [3-5]. Though the tumor usually presents as a large liver tumor in an adult, a giant (> 10 cm) and hanging tumor arising from the Reidel's lobe of the liver over a narrow stalk is very unusual and has not been reported in literature to date. We describe a case of a 29-year-old young female with a short clinical course and resectable hanging UESL, but unfortunately developed early recurrence despite R0 resection, signifying a poor prognosis disease.