Acute aortic dissection in a patient with Marfan syndrome during advanced pregnancy

摘要

Pregnant patients with Marfan syndrome (MFS) are at high risk of developing aortic dissection or rupture during the third trimester and early postpartum period. This increased likelihood is the consequence of the hyperdynamic and hypervolemic cardiocirculatory state and/or pregnancy-mediated structural changes of the arterial wall in response to hemodynamic and hormonal changes. In this article, we report on the case of a 26-year-old pregnant woman with MFS in the 30th gestation week, who presented with type A aortic dissection at the emergency department. According to the multidisciplinary team decision, an urgent cesarean section was performed, followed by the Bentall procedure. The patient was discharged on the 10th postoperative day, and her premature child was discharged 6 weeks after birth.