Acquired hepatocerebral degeneration with middle cerebellar peduncles lesions: Case report and review of the literature

摘要

Acquired hepatocerebral degeneration (AHD) is a progressive neurological syndrome characterized by parkinsonism, ataxia, and other movement disorders caused by various progressive liver diseases, especially those characterized by portosystemic shunt [1,2]. Cerebellaj symptoms such as pathological cerebellar changes are observed in some patients with AHD; however, cerebellar lesions, especially in the middle cerebellar peduncles (MCP), are rarely observed on brain MR imaging [3,4]. We found MCP lesions in an AHD patient whose cerebellar symptoms completely disappeared and whose MCP lesions reduced after balloon-occluded retrograde transveneous obliteration (BRTO) for the portosystemic shunt. We successfully followed the chronological changes of these lesions in response to the treatment.