Cardiac magnetic resonance findings in congenitally absent pericardium.

摘要

A 58-year-old man with no relevant past or family history was referred after a 1-month history of palpitations. Electrocardiography demonstrated left axis deviation and right ventricular (RV) outflow-type ectopic beats (A). Echocardiography revealed a laterally displaced heart with unusual RV appearance. Axial Tl-weighted cardiac magnetic resonance imaging demonstrates the heart displaced into the left hemi-thorax (B), with absent pericardium (grey arrow) and normal RV volumes (end-diastolic volume 150 ml, end-systolic volume 70 ml, ejection fraction 53%). Left ventricular (LV) volumes, mass, and function were normal. A characteristic lingula of lung tissue (white arrow) is interposed between the aorta (AA) and main pulmonary artery (MPA) (C)-a pathognomonic finding in congenitally absent pericardium.