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Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society

Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society

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中文名称：囊性纤维化杂志：欧洲囊性纤维化学会官方杂志

ISSN：1569-1993
出版周期：-

发文量：1232

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1.Does current reporting of lung function by the UK cystic fibrosis registry allow a fair comparison of adult centres?

机译：当前英国囊性纤维化登记处的肺功能报告允许公平比较成人中心吗？
- 作者：Julia Anne Nightingale;Clive Osmond
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
- Cystic fibrosis;
- Clinical epidemiology;
- Respiratory measurement;
2.Interpretation of Cystic Fibrosis Centre rankings: Meaningful comparisons or biased statistics?

机译：解释囊性纤维化中心排名：有意义的比较或偏见统计数据？
- 作者：Sanja Stanojevic
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
3.Investigating the variation in the incidence of new Pseudomonas aeruginosa infection between paediatric cystic fibrosis centres

机译：调查小儿囊性纤维化中心新假单胞菌铜绿假单胞菌感染发生率的变异
- 作者：F.J. Gilchrist;A.M. Jones;A.R. Smyth;K.W. Southern;A.K. Webb;W. Lenney
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
- Cystic fibrosis;
- Microbiology;
- Paediatrics;
- Pseudomonas aeruginosa;
4.Peripheral muscle abnormalities in cystic fibrosis: Etiology, clinical implications and response to therapeutic interventions

机译：囊性纤维化外周肌异常：病因，临床意义和对治疗干预的反应
- 作者：Mathieu Gruet;Thierry Troosters;Samuel Verges
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
- Cystic fibrosis;
- Muscle function;
- Exercise interventions;
- Aerobic function;
- CFTR;
- Nutritional status;
- Muscle metabolism;
5.Liver disease in cystic fibrosis presents as non-cirrhotic portal hypertension

机译：肝病在囊性纤维化呈非肝硬化门骨菌
- 作者：Peter Witters;Louis Libbrecht;Tania Roskams;Kris De Boeck;Lieven Dupont;Marijke Proesmans;Fran?ois Vermeulen;Geert Maleux;Diethard Monbaliu;Jacques Pirenne;David Cassiman
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
6.Acetic acid is elevated in the exhaled breath of cystic fibrosis patients

机译：醋酸在呼出的囊性纤维化患者中升高
- 作者：Patrik ?paněl;Kristyna Sovová;Kseniya Dryahina;Tereza Dou?ová;Pavel D?evínek;David Smith
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
7.A first step to STOP cystic fibrosis exacerbations

机译：停止囊性纤维化恶化的第一步
- 作者：Pierre-Régis Burgel;David W. Reid;Shawn D. Aaron
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
8.High incidence of non-tuberculous mycobacteria-positive cultures among adolescent with cystic fibrosis

机译：青少年非结核分枝杆菌阳性培养物的高发病率，囊性纤维化
- 作者：Zoé Cavalli;Quitterie Reynaud;Romain Bricca;Rapha?le Nove-Josserand;Stéphane Durupt;Philippe Reix;Marie Perceval;Michèle Pérouse de Montclos;Gérard Lina;Isabelle Durieu
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
- Cystic fibrosis;
- Mycobacterium avium;
- Mycobacterium abscessus;
- Non-tuberculous mycobacteria;
- Pulmonary disease;
9.Take it to the Bank

机译：把它带到银行
- 作者：J.P. Clancy;Elizabeth Joseloff
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
10.Continuous glucose monitoring in a cystic fibrosis patient to predict pulmonary exacerbation?

机译：在囊性纤维化患者中连续葡萄糖监测预测肺部加剧？
- 作者：T.B. Inman;J.A. Proudfoot;M. Lim;C. Demeterco-Berggren
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
- Cystic fibrosis;
- Diabetes;
- Impaired glucose tolerance;
- Continuous glucose monitoring;
11.Pulmonary surfactant dysfunction in pediatric cystic fibrosis: Mechanisms and reversal with a lipid-sequestering drug

机译：小儿囊性纤维化的肺表面活性剂功能障碍：用脂质螯合药物的机制和逆转
- 作者：Lasantha Gunasekara;Mustafa Al-Saiedy;Francis Green;Ryan Pratt;Candice Bjornson;Ailian Yang;W. Michael Schoel;Ian Mitchell;Mary Brindle;Mark Montgomery;Elizabeth Keys;John Dennis;Grishma Shrestha;Matthias Amrein
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第5期
- Cystic fibrosis;
- Lung surfactant;
- Cholesterol;
- oxidative stress;
- Surface tension;
- Phospholipids;
- Free fatty acids;
- Inflammation;
- Infection;
- Genotypes;
12.A single bout of maximal exercise improves lung function in patients with cystic fibrosis

机译：一个最大锻炼的单一Bout在囊性纤维化患者中改善了肺功能
- 作者：Matthew A. Tucker;Reva Crandall;Nichole Seigler;Paula Rodriguez-Miguelez;Kathleen T. McKie;Caralee Forseen;Jeffrey Thomas;Ryan A. Harris
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Spirometry;
- Impulse oscillometry;
- Exercise capacity;
- Multi-breath washout;
13.What keeps children with cystic fibrosis awake at night?

机译：晚上让孩子保持囊性纤维化症？
- 作者：Moya Vandeleur;Lisa M. Walter;David S. Armstrong;Philip Robinson;Gillian M. Nixon;Rosemary S.C. Horne
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Sleep;
- Actigraphy;
- Oximetry;
- Sleep hygiene;
14.News

机译：消息
- 作者：Diana Bilton
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
15.Tracheal diverticula in advanced cystic fibrosis: Prevalence, features, and outcomes after lung transplantation

机译：晚期囊性纤维化的气管憩室：肺移植后的患病率，特征和结果
- 作者：Siddhartha G. Kapnadak;Gregory A. Kicska;Kathleen J. Ramos;Desiree A. Marshall;Tamara Y. Carroll;Sudhakar N. Pipavath;Michael S. Mulligan;Christopher H. Goss;Moira L. Aitken
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Lung transplantation;
- Cystic fibrosis;
- Tracheal diverticulum;
- Lung diseases;
- Pseudomonas infections;
- Tomography;
- x-ray computed;
16.Increased risk of PTLD in lung transplant recipients with cystic fibrosis

机译：肺移植受者的PTLD风险增加，囊性纤维化
- 作者：Erin M. Lowery;William Adams;Shellee A. Grim;Nina M. Clark;Leah Edwards;Jennifer E. Layden
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Post transplant lymphoproliferative disorder;
- Cystic fibrosis;
- Ebstein–Barr virus;
17.Editorial Board

机译：编辑委员会
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
18.The 1-min sit-to-stand test in cystic fibrosis — Insights into cardiorespiratory responses

机译：囊性纤维化1分钟的静态测试 - 洞察力反应
- 作者：Thomas Radtke;Helge Hebestreit;Milo A. Puhan;Susi Kriemler
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Exercise testing;
- Validity;
- Lung disease;
- Functional capacity;
19.Real-life acute lung function changes after lumacaftor/ivacaftor first administration in pediatric patients with cystic fibrosis

机译：在囊性纤维化患者中洛马飞舵/ IVACAFTOR首次施用后现实急性肺功能变化
- 作者：Aurélie Labaste;Camille Ohlmann;Catherine Mainguy;Virginie Jubin;Marie Perceval;Laurianne Coutier;Philippe Reix
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Lumacaftor;
- Modulators;
- Cystic fibrosis;
- Acute;
- Airway obstruction;
- Bronchoconstriction;
- Pediatric;
20.A treatment evaluator tool to monitor the real-world effectiveness of inhaled aztreonam lysine in cystic fibrosis

机译：一种治疗评估工具，以监测吸入的Aztreonam赖氨酸在囊性纤维化中的真实效力
- 作者：Barry J Plant;Damian G Downey;Joe A Eustace;Cedric Gunaratnam;Charles S Haworth;Andrew M Jones;Edward F McKone;Daniel G Peckham;R. Ian Ketchell;Diana Bilton
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Aztreonam;
- Cystic fibrosis;
- Forced expiratory volume;
- Evaluation tool;
- Intravenous antibiotics;
21.Bicarbonate in cystic fibrosis

机译：碳酸氢盐在囊性纤维化
- 作者：Karl Kunzelmann;Rainer Schreiber;Hans Beat Hadorn
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Mucoviscidosis;
- Cystic fibrosis;
- Bicarbonate;
- Mucus;
- Cystic fibrosis transmembrane conductance regulator;
- CFTR;
22.Comment on data sparsity - Diagnostic and prognostic significance of systemic alkyl quinolones for P. aeruginosa in cystic fibrosis: A longitudinal study

机译：评评关于数据稀疏性 - 孢子纤维化铜绿假素全身烷基喹诺酮类的诊断与预后意义：纵向研究
- 作者：Erfan Ayubi;Jamal Hallajzadeh;Saeid Safiri
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Cystic fibrosis;
- P. aeruginosa;
- Bias;
- Sparse data;
- Penalization;
23.Validation of multiple breath washout devices

机译：验证多次呼吸冲洗装置
- 作者：Lena Raaijmakers;Renee Jensen;Sanja Stanojevic;Felix Ratjen
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
24.Learning’s from the Editors Desk – 2017

机译：学习从编辑服务台 - 2017年
- 作者：Scott C. Bell;Carlo Castellani;Patrick A. Flume
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
25.Diagnostic and prognostic significance of systemic alkyl quinolones for P. aeruginosa in cystic fibrosis: A longitudinal study; response to comments

机译：铜绿假单胞菌在囊性纤维化中的诊断和预后意义：纵向研究; 回应评论
- 作者：H.L. Barr;N. Halliday;D.A. Barrett;P. Williams;D.L. Forrester;D. Peckham;K. Williams;A.R. Smyth;D. Honeybourne;J.L. Whitehouse;E.F. Nash;J. Dewar;A. Clayton;A.J. Knox;M. Cámara;A.W. Fogarty
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
26.Corrigendum to “WS04.1 The effect of Orkambi? on exercise capacity and muscle strength” [J Cyst Fibros, volume 16, supplement 1, June 2017, pages S6–S7]

机译：勘误将“WS04.1 Orkambi的效果？运动能力和肌肉力量“[J Cyst纤维，第16卷，补充1，2017年6月，页面S6-S7]
- 作者：R. Buckley;C.M. Reilly;S. Kelly;E. Ward;C. OConnor;S. Carter;C.G. Gallagher;E.F. McKone
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
27.The potential of phage therapy in cystic fibrosis: Essential human-bacterial-phage interactions and delivery considerations for use in Pseudomonas aeruginosa -infected airways

机译：囊性纤维化噬菌体疗法的潜力：必需的人体细菌 - 噬菌体相互作用和递送考虑，适用于铜绿假单胞菌的铜绿素 - 富集的气道
- 作者：Stephanie Trend;Angela M. Fonceca;William G. Ditcham;Anthony Kicic;AREST CF
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Cystic fibrosis;
- Bacteriophage;
- Phage therapy;
- Infection;
- Pseudomonas aeruginosa;
- Antimicrobial;
28.Inhaled ENaC antisense oligonucleotide ameliorates cystic fibrosis-like lung disease in mice

机译：吸入的ENAC反义寡核苷酸在小鼠中改善囊性纤维化样肺病
- 作者：Jeff R. Crosby;Chenguang Zhao;Chong Jiang;Dong Bai;Melanie Katz;Sarah Greenlee;Hiroshi Kawabe;Michael McCaleb;Daniela Rotin;Shuling Guo;Brett P. Monia
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Cystic fibrosis;
- ENaC;
- Antisense oligonucleotide;
- Aerosol;
29.Corrigendum to “Does current reporting of lung function by the UK cystic fibrosis registry allow a fair comparison of adult centres?” [J Cyst Fibros (2017) 585–591]

机译：“英国囊性纤维化登记处的勘察”目前的肺功能报告患者允许公平比较成人中心吗？“ [J Cyst Fibros（2017）585-591]
- 作者：J.A. Nightingale;C. Osmond
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
30.New Comorbidities in the Changing Face of Cystic Fibrosis Care

机译：在囊性纤维化护理的变化面孔中的新融合
- 作者：Michael Bonk;Michael M. Rey;Denis Hadjiliadis
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
31.Bile salt stimulated lipase: Inhibition by phospholipids and relief by phospholipase A 2

机译：胆汁盐刺激脂肪酶：磷脂抑制和磷脂酶a 2的抑制作用
- 作者：Elena Venuti;Dmitry Shishmarev;Philip W. Kuchel;Shoma Dutt;Caron S. Blumenthal;Kevin J. Gaskin
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Bile salt stimulated lipase;
- Cystic fibrosis;
- Enzyme therapy;
- NMR spectroscopy;
- Pancreatic insufficiency;
- Titrimetric enzyme assay;
32.Exercise assessment and training in cystic fibrosis: Can less achieve more?

机译：运动评估和患囊性纤维化的培训：可以少达到更多吗？
- 作者：Narelle S. Cox;Anne E. Holland
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
33.A 3-year prognostic score for adults with cystic fibrosis

机译：具有囊性纤维化的成年人的3年预后分数
- 作者：L. Nkam;J. Lambert;A. Latouche;G. Bellis;PR. Burgel;M.N. Hocine
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Cystic fibrosis;
- Prognostic factors;
- Registry data;
- Logistic model;
- Prognostic score;
34.Pregnancy among cystic fibrosis women in the era of CFTR modulators

机译：CFTR调制器时代囊性纤维化妇女的怀孕
- 作者：Sonya L. Heltshe;Emily M. Godfrey;Tatiana Josephy;Moira L. Aitken;Jennifer L. Taylor-Cousar
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Pregnancy;
- G551D;
- Ivacaftor;
- Lumacaftor;
35.Increased prevalence of colonic adenomas in patients with cystic fibrosis

机译：囊性纤维化患者结肠腺瘤的流行增加
- 作者：Mehdi Hegagi;Shawn D. Aaron;Paul James;Rakesh Goel;Avijit Chatterjee
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2017年第6期
- Colonoscopy;
- Cystic fibrosis;
- Adenoma;
36.The CF-CARES primary palliative care model: A CF-specific structured assessment of symptoms, distress, and coping

机译：CF-Cares初级姑息治疗模型：症状，痛苦和应对的CF特异性结构评估
- 作者：Deborah Friedman;Rachel W. Linnemann;Lily L. Altstein;Suhayla Islam;Kieu-Tram Bach;Chelsea Lamb;John Volpe;Caitlin Doolittle;Anita St. John;Patricia J. OMalley;Gregory S. Sawicki;Anna M. Georgiopoulos;Lael M. Yonker;Samuel M. Moskowitz
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Cystic fibrosis;
- Palliative care;
- Chronic symptom burden;
- Symptom prevalence;
- Depression;
- Anxiety;
37.Faecal calprotectin concentrations in young children with cystic fibrosis

机译：粪便钙蛋白浓度在患有囊性纤维化的幼儿
- 作者：Helmut Ellemunter;Katharina Schüller;Gratiana Steinkamp
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
38.Let's talk about sex: Behaviors, experience and health care utilization in young women with CF

机译：让我们谈谈性别：CF的年轻女性的行为，经验和医疗利用
- 作者：Sonya L. Heltshe;Jennifer L. Taylor-Cousar
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
39.News

机译：消息
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
40.Caregiver burden of parents of young children with cystic fibrosis

机译：患有囊性纤维化的幼儿父母的照顾者负担
- 作者：C. Fitzgerald;S. George;R. Somerville;B. Linnane;P. Fitzpatrick
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Caregiver burden;
- CarerQol;
- Cystic fibrosis;
- Parents;
41.Age-related levels of fecal M2-pyruvate kinase in children with cystic fibrosis and healthy children 0 to 10years old

机译：囊性纤维化和健康儿童0至10年龄的儿童粪便M2-丙酮酸激酶与年龄相关水平。
- 作者：Millie Garg;Steven T. Leach;Tamara Pang;Bronwen Needham;Michael J. Coffey;Tamarah Katz;Roxanne Strachan;John Widger;Penelope Field;Yvonne Belessis;Sandra Chuang;Andrew S. Day;Adam Jaffe;Chee Y. Ooi
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Biomarkers;
- Pyruvate kinase;
- Intestinal neoplasms;
- Cystic fibrosis;
- Gastrointestinal inflammation;
- Pediatrics;
42.The use of fructosamine in cystic fibrosis-related diabetes (CFRD) screening

机译：使用果糖胺在囊性纤维化相关糖尿病（CFRD）筛查中
- 作者：Grace Y. Lam;Michelle Doll-Shankaruk;Jan Dayton;Karina Rodriguez-Capote;Trefor N. Higgins;Dylan Thomas;Kimberley Mulchey;Maeve P. Smith;Neil E. Brown;Winnie M. Leung;Mathew P. Estey
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Cystic fibrosis-related diabetes;
- Serum fructosamine;
- Screening;
- Oral glucose tolerance test;
- FEV1;
43.Retrospective observational study of French patients with cystic fibrosis and a Gly551Asp- CFTR mutation after 1 and 2years of treatment with ivacaftor in a real-world setting

机译：法国囊性纤维化患者的回顾性观测研究1和2年后的IVACAFTOR在真实世界环境中治疗后的1和2年的突变突变
- 作者：Dominique Hubert;Clémence Dehillotte;Anne Munck;Valérie David;Jinmi Baek;Laurent Mely;Stéphane Dominique;Sophie Ramel;Isabelle Danner Boucher;Sylvaine Lefeuvre;Quitterie Reynaud;Virginie Colomb-Jung;Prissile Bakouboula;Lydie Lemonnier
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Cystic fibrosis;
- CFTR modulators;
- Lumacaftor;
44.Analytical and biological variation in repeated sweat chloride concentrations in clinical trials for CFTR modulator therapy

机译：CFTR调节剂治疗临床试验中反复汗液浓度的分析和生物变化
- 作者：V.A. LeGrys;T.C. Moon;J. Laux;M.J. Rock;F. Accurso
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Analytical variation;
- Biological variation;
- Cystic fibrosis;
- Index of individuality;
- Reference change value;
- Sweat chloride;
45.Editorial Board

机译：编辑委员会
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
46.Antibiotic exposure and interpersonal variance mask the effect of ivacaftor on respiratory microbiota composition

机译：抗生素暴露和人际关系差异掩模IVACAFTOR对呼吸微生物群组合物的影响
- 作者：Anton Y. Peleg;Jocelyn M. Choo;Katherine M. Langan;Deirdre Edgeworth;Dominic Keating;John Wilson;Geraint B. Rogers;Tom Kotsimbos
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Respiratory microbiome;
- Ivacaftor;
- Antibiotics;
47.Complications of long and intermediate term venous catheters in cystic fibrosis patients: A multicenter study

机译：囊性纤维化患者长期和中期静脉导管的并发症：多中心研究
- 作者：Teresa L. May;Alex H. Gifford;Thomas Lahiri;Adam Black;Janet Trang;Alexandra G. Cornell;Karyll Gonzalez;Scott Morin;Mark Napier;Christine W. Duarte;Jonathan B. Zuckerman
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Central line;
- Infectious complications;
- Pulmonary exacerbation;
- CFF Patient Registry;
48.Is there an association between back pain and stress incontinence in adults with cystic fibrosis? A retrospective cross-sectional study

机译：是否存在患有囊性纤维化的成年人的背部疼痛和压力尿失禁之间存在关联？回顾性横截面研究
- 作者：Jane E. Ashbrook;Carol Shacklady;Sue Johnson;Gillian Yeowell;Peter Charles Goodwin
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Cystic fibrosis;
- Back pain;
- Stress urinary incontinence;
- Lung function;
- Cross sectional study;
49.The relationship between sweat chloride levels and mortality in cystic fibrosis varies by individual genotype

机译：患者氯化物水平与囊性纤维化中死亡率之间的关系因个体基因型而异
- 作者：Julia C. Espel;Hannah L. Palac;Ankit Bharat;Joanne Cullina;Michelle Prickett;Marc Sala;Susanna A. McColley;Manu Jain
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Cystic fibrosis;
- Sweat chloride;
- Mortality;
- CFTR genotype;
- Mutation;
50.Gene editing & stem cells

机译：基因编辑＆amp; 干细胞
- 作者：Patrick T. Harrison;Nils Hoppe;Ulrich Martin
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Gene editing;
- Stem cells;
- Drug screening;
- Ethics;
- iPS cells;
51.Recovery of lung function following a pulmonary exacerbation in patients with cystic fibrosis and the G551D - CFTR mutation treated with ivacaftor

机译：囊性纤维化患者肺部加剧后肺功能回收肺功能和IVACAFTOR处理的G551D - CFTR突变
- 作者：Patrick A. Flume;Claire E. Wainwright;D. Elizabeth Tullis;Sally Rodriguez;Minoo Niknian;Mark Higgins;Jane C. Davies;Jeffrey S. Wagener
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
52.Exercise and its varied impact on airway dynamics

机译：运动及其不同影响的气道动态
- 作者：Daniel Stevens
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
53.Fecal calprotectin concentrations in young children with cystic fibrosis: Authors response

机译：患有囊性纤维化的幼儿中的粪便抗蛋白酶浓度：作者反应
- 作者：Millie Garg;Steven T. Leach;Andrew S. Day;Chee Y. Ooi
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Leukocyte L1 antigen complex;
- Calprotectin;
- S100 proteins;
- Cystic fibrosis;
- Gastrointestinal inflammation;
- Pediatrics;
54.Combined lung-liver-pancreas transplantation in a recipient with cystic fibrosis

机译：患有囊性纤维化的受体中的肺肝胰腺移植组合
- 作者：A.S. Barbas;M.J. Dib;D.P. Al-Adra;N. Goldaracena;G. Sapisochin;T.K. Waddell;S. Keshavjee;N. Selzner;C. Chaparro;M.S. Cattral
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
55.Multiple prevalent fractures in relation to macroscopic bone architecture in patients with cystic fibrosis

机译：囊性纤维化患者宏观骨结构相关的多种普遍性骨折
- 作者：Mirjam Stahl;Christian Holfelder;Carolin Kneppo;Meinhard Kieser;Christian Kasperk;Eckhard Schoenau;Olaf Sommerburg;Burkhard T?nshoff
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Cystic fibrosis;
- Bone disease;
- Fracture rate;
- Macroscopic bone architecture;
- Bone densitometry;
- Noninvasive monitoring;
56.Detection of CFTR function and modulation in primary human nasal cell spheroids

机译：检测初级人鼻腔球体中CFTR功能和调制
- 作者：John J. Brewington;Erin T. Filbrandt;F.J. LaRosa;Alicia J. Ostmann;Lauren M. Strecker;Rhonda D. Szczesniak;John P. Clancy
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- CFTR;
- Organoid;
- Modulator;
- Personalized model system;
57.Sexual and reproductive health care utilization and preferences reported by young women with cystic fibrosis

机译：患有囊性纤维化的年轻女性报告的性和生殖保健利用和偏好
- 作者：Traci M. Kazmerski;Gregory S. Sawicki;Elizabeth Miller;Kelley A. Jones;Kaleab Z. Abebe;Lisa K. Tuchman;Sigrid Ladores;Ronald C. Rubenstein;Scott D. Sagel;Daniel J. Weiner;Joseph M. Pilewski;David M. Orenstein;Sonya Borrero
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Sexual and reproductive health;
- Women's health;
- Cystic fibrosis;
58.Advancing the GI frontier for patients with CF

机译：推进CF患者的GI边疆
- 作者：Steven D. Freedman;Michael Wilschanski;Sarah Jane Schwarzenberg
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
59.Another step in the journey: From CFTR mutation to sweat chloride concentration to survival

机译：旅程中的另一步：从CFTR突变到汗液氯化物浓度以存活
- 作者：D.R. VanDevanter;N. Mayer-Hamblett
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
60.Drugs during pregnancy and breast feeding in women diagnosed with Cystic Fibrosis - An update

机译：怀孕期间的药物和患有囊性纤维化的女性母乳喂养 - 更新
- 作者：M.A.G.M. Kroon;A.M. Akkerman-Nijland;B.L. Rottier;G.H. Koppelman;O.W. Akkerman;D.J. Touw
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Cystic Fibrosis;
- Pregnancy;
- Breast feeding;
- CFTR modulators;
61.Comparing the management of constipation and distal intestinal obstruction syndrome between paediatricians and adult physicians

机译：比较儿科医生与成人医师之间便秘和远端肠梗阻综合征的管理
- 作者：J.A. Green;W.D. Carroll;F.J. Gilchrist
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Constipation;
- Cystic fibrosis;
- Distal intestinal obstruction syndrome;
- Laxatives;
62.Sexual and reproductive health behaviors and experiences reported by young women with cystic fibrosis

机译：患有囊性纤维化的年轻女性报告的性和生殖健康行为和经验
- 作者：Traci M. Kazmerski;Gregory S. Sawicki;Elizabeth Miller;Kelley A. Jones;Kaleab Z. Abebe;Lisa K. Tuchman;Sigrid Ladores;Ronald C. Rubenstein;Scott D. Sagel;Daniel J. Weiner;Joseph M. Pilewski;David M. Orenstein;Sonya Borrero
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第1期
- Sexual and reproductive health;
- Women's health;
- Cystic fibrosis;
63.Three-center feasibility of lung clearance index in infants and preschool children with cystic fibrosis and other lung diseases

机译：婴儿和学龄前儿童患有囊性纤维化和其他肺病的肺部清关指数的三中心可行性
- 作者：Stahl Mirjam;Graeber Simon Y.;Joachim Cornelia;Barth Sandra;Ricklefs Isabell;Diekmann Gesa;Kopp Matthias V.;Naehrlich Lutz;Mall Marcus A.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Lung clearance index;
- Multiple breath washout;
- Infant lung function test;
- Early CF lung disease;
- Clinical trial endpoint;
64.Ivacaftor restores CFTR-dependent sweat gland fluid secretion in cystic fibrosis subjects with S945L alleles

机译：IVAcaftor用S945L等位基因恢复CFTR依赖性汗腺液体分泌物中的囊性纤维化受试者
- 作者：Kim Jeeyeon;Davies Zoe;Dunn Colleen;Wine Jeffrey J.;Milla Carlos
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Sweat rate;
- S945L mutation;
- Residual function CFTR mutation;
- CFTR modulators;
65.Effect of Lumacaftor/Ivacaftor on glucose metabolism and insulin secretion in Phe508del homozygous cystic fibrosis patients

机译：Lumacafacer / IVAcaftor对PHE508del纯合囊性纤维化患者葡萄糖代谢和胰岛素分泌的影响
- 作者：Thomassen Jan C.;Mueller Matthias I.;Alcazar Miguel A. Alejandre;Rietschel Ernst;van Koningsbruggen-Rietschel Silke
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- Insulin secretion;
- Glucose metabolism;
- Lumacaftor/Ivacaftor;
- OGTT;
- IVGTT;
- Homozygous Phe508del;
66.Up-to-date and projected estimates of survival for people with cystic fibrosis using baseline characteristics: A longitudinal study using UK patient registry data

机译：使用基线特征的囊性纤维化患者的最新和预计的生存估计：使用英国患者注册表数据进行纵向研究
- 作者：Keogh Ruth H.;Szczesniak Rhonda;Taylor-Robinson David;Bilton Diana
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- CFTR genotype;
- Cystic fibrosis;
- Flexible parametric survival model;
- Longitudinal study;
- Patient registry;
- Survival;
67.ECFS best practice guidelines: the 2018 revision

机译：ECFS最佳实践指南：2018年修订版
- 作者：Castellani Carlo;Duff Alistair J. A.;Bell Scott C.;Heijerman Harry G. M.;Munck Anne;Ratjen Felix;Sermet-Gaudelus Isabelle;Southern Kevin W.;Barben Jurg;Flume Patrick A.;Hodkova Pavia;Kashirskaya Nataliya;Kirszenbaum Maya N.;Madge Sue;Oxley Helen;Plant Barry;Schwarzenberg Sarah Jane;Smyth Alan R.;Taccetti Giovanni;Wagner Thomas O. F.;Wolfe Susan P.;Drevinek Pavel
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- Standards of care;
- Multidisciplinary management;
- Best practice;
- Guidelines;
- Consensus;
68.Lumacaftor/ivacaftor in patients with cystic fibrosis and advanced lung disease homozygous for F508del-CFTR

机译：Lumacafetor / Ivacafacter在囊性纤维化患者中和F508del-CFTR纯合的先进肺病
- 作者：Taylor-Cousar Jennifer L.;Jain Manu;Barto Tara Lynn;Haddad Tarik;Atkinson Jeffrey;Tian Simon;Tang Rui;Marigowda Gautham;Waltz David;Pilewski Joseph
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- F508del;
- Lumacaftor;
- Ivacaftor;
- Severe lung dysfunction;
- Advanced lung disease;
69.Mechanisms of humoral immune response against Pseudomonas aeruginosa biofilm infection in cystic fibrosis

机译：对孢子铜绿假单胞菌孢子纤维化症铜绿假单胞菌感染的体液免疫应答机制
- 作者：Mauch Renan Marrichi;Jensen Peter Ostrup;Moser Claus;Levy Carlos Emilio;Hoiby Niels
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- Pseudomonas aeruginosa;
- Lung infection;
- Humoral immune response;
- Antibodies;
70.A comorbidity of CF in need of our attention and activity: Attention Deficit Hyperactivity Disorder!

机译：需要我们的注意力和活动的CF合并症：注意力缺陷多动障碍！
- 作者：Lemiere Jurgen;Havermans Trudy
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
71.16S rRNA gene sequencing reveals site-specific signatures of the upper and lower airways of cystic fibrosis patients

机译：16S RRNA基因测序显示囊性纤维化患者的上下气道的特异性特异性签名
- 作者：Lucas Sarah K.;Yang Robert;Dunitz Jordan M.;Boyer Holly C.;Hunter Ryan C.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Chronic sinusitis;
- Microbiome;
- Microbial ecology;
- Mucus;
72.Ratiometric sweat secretion optical test in cystic fibrosis, carriers and healthy subjects

机译：囊性纤维化，载体和健康受试者的比例汗液分泌光学试验
- 作者：Bergamini Gabriella;Tridello Gloria;Calcaterra Elisa;Ceri Stefano;Tagliasacchi Marco;Bianchi Federico;Monti Federico;Masciadri Andrea;Laudanna Eugenia;Peserico Denise;Sorio Elena;Esposito Valeria;Leal Teresinha;Assael Baroukh Maurice;Sorio Claudio;Melotti Paola
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- Sweat rate;
- Image analysis;
- Cystic fibrosis transmembrane conductance regulator;
- Sweat glands;
73.The effect of enteral tube feeding in cystic fibrosis: A registry based study

机译：肠内饲喂在囊性纤维化中的影响：基于注册表的研究
- 作者：Libeert Denis;Declercq Dimitri;Wanyama Simeon;Thomas Muriel;Van Daele Sabine;De Baets Frans;Van Biervliet Stephanie
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- Tube feeding;
- Gastrostomy;
- Malnutrition;
- Pulmonary function;
74.New directions on lung clearance index variability and feasibility

机译：关于肺部清关指数变异性和可行性的新方向
- 作者：ONeill Katherine;Saunders Clare
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
75.Blood flow regulation and oxidative stress during submaximal cycling exercise in patients with cystic fibrosis

机译：囊性纤维化患者血流循环运动中血流调节和氧化应激
- 作者：Tucker Matthew A.;Berry Breana;Seigler Nichole;Davison Gareth W.;Quindry John C.;Eidson Dabney;McKie Kathleen T.;Harris Ryan A.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
76.FAM13A is a modifier gene of cystic fibrosis lung phenotype regulating rhoa activity, actin cytoskeleton dynamics and epithelial-mesenchymal transition

机译：FAM13A是囊性纤维化肺表型调节RHOA活性的改性剂基因，肌动蛋白细胞骨架动力学和上皮 - 间充质转换
- 作者：Corvol Harriet;Rousselet Nathalie;Thompson Kristin E.;Berdah Laura;Cottin Guillaume;Foussigniere Tobias;Longchampt Elisabeth;Fiette Laurence;Sage Edouard;Prunier Celine;Drumm Mitchell;Hodges Craig A.;Boelle Pierre-Yves;Guillot Loic
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- Modifier genes;
- FAM13A;
77.A guide to interpreting estimated median age of survival in cystic fibrosis patient registry reports

机译：解释核心纤维化患者登记报告中估计生存中位年龄的指南
- 作者：Keogh Ruth H.;Stanojevic Sanja
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Annual report;
- Birth cohort;
- Conditional survival;
- Median survival;
- Patient registry;
- Period estimates;
- UK Cystic Fibrosis Registry;
78.In statistics we trust: Towards the careful derivation and interpretation of meaningful survival estimates in cystic fibrosis

机译：在统计数据中，我们信任：致力于仔细的衍生和解释囊性纤维化中的有意义的存活估计
- 作者：Mayer-Hamblett N.;Polineni D.;Heltshe S. L.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
79.Variability of monthly nitrogen multiple-breath washout during one year in children with cystic fibrosis

机译：囊性纤维化儿童一年内每月氮素多口呼吸冲洗的可变性
- 作者：Green Kent;Kongstad Thomas;Skov Marianne;Buchvald Frederik;Rosthoj Susanne;Marott Jacob Louis;Gustafsson Per;Pressler Tacjana;Nielsen Kim Gjerum
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- Paediatrics;
- Lung function;
- Nitrogen multiple-breath washout;
- Lung clearance index;
- LCI;
80.Screening for ADHD in adults with cystic fibrosis: Prevalence, health-related quality of life, and adherence

机译：患有囊性纤维化的成人中的ADHD：患病率，与健康相关的生活质量和依从性
- 作者：Georgiopoulos Anna M.;Friedman Deborah;Porter Elizabeth A.;Krasner Amy;Kakarala Sheetal P.;Glaeser Breanna K.;Napoleon Siena C.;Wozniak Janet
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- Attention-deficit hyperactivity disorder;
- Health-related quality of life;
- Adherence;
81.Variability of lung clearance index in clinically stable cystic fibrosis lung disease in school age children

机译：学龄儿童临床稳定囊性纤维化肺病中肺部清除指标的变异性
- 作者：Svedberg Marcus;Gustafsson Per M.;Robinson Paul D.;Rosberg Monica;Lindblad Anders
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- Multiple breath washout;
- Lung clearance index;
- Pulmonary exacerbation;
82.Attention deficit hyperactivity disorder symptoms in patients with cystic fibrosis

机译：囊性纤维化患者的注意力缺陷多动障碍症状
- 作者：Cohen-Cymberknoh Malena;Tanny Tzlil;Breuer Oded;Blau Hannah;Mussaffi Huda;Kadosh Diana;Gartner Silvia;Salinas Alma;Bentur Lea;Nir Vered;Gur Michal;Reiter Joel;Shoseyov David;Kerem Eitan;Berger Itai
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第2期
- Cystic fibrosis;
- ADHD;
- Adherence;
- Chronic illness;
- Inflammatory disease;
83.Prevalence of hypoglycemia during oral glucose tolerance testing in adults with cystic fibrosis and risk of developing cystic fibrosis-related diabetes

机译：具有囊性纤维化囊性纤维化的口腔葡萄糖耐受性测试中低血糖症的患病率及发育囊性纤维化相关糖尿病的风险
- 作者：Mannik Lisa A.;Chang Kristy A.;Annoh Pascalyn Q. K.;Sykes Jenna;Gilmour Julie;Robert Ronalee;Stephenson Anne L.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Cystic fibrosis;
- Hypoglycemia;
- Diabetes mellitus;
- Glucose tolerance test;
84.Insights into the cystic fibrosis care in Eastern Europe: Results of survey

机译：东欧囊性纤维化护理的见解：调查结果
- 作者：Walicka-Serzysko Katarzyna;Peckova Monika;Noordhoek Jacquelien J.;Sands Dorota;Drevinek Pavel
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Cystic fibrosis;
- Standards of care;
- Eastern Europe;
85.Pulmonary exacerbations and acute declines in lung function in patients with cystic fibrosis

机译：囊性纤维化患者肺功能肺功能和急性下降
- 作者：Wagener Jeffrey S.;Williams Michael J.;Millar Stefanie J.;Morgan Wayne J.;Pasta David J.;Konstan Michael W.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Cystic fibrosis;
- Pulmonary exacerbations;
- Lung function;
86.Back to the source - Modern insights into pulmonary exacerbations and lung function decline from CF registry data

机译：返回源 - 从CF注册表数据中触及肺硬化和肺功能下降的现代洞察力
- 作者：Rayment Jonathan H.;Quon Bradley S.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
87.The association between Staphylococcus aureus and subsequent bronchiectasis in children with cystic fibrosis

机译：囊性纤维化儿童金黄色葡萄球菌和后续支气管切除症的关系
- 作者：Caudri Daan;Turkovic Lidija;Ng Jolyn;de Klerk Nicholas H.;Rosenow Tim;Hall Graham L.;Ranganathan Sarath C.;Sly Peter D.;Stick Stephen M.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- CT scan;
- Structural lung damage;
- Infection and inflammation;
- Lung function;
88.Early life growth patterns persist for 12 years and impact pulmonary outcomes in cystic fibrosis

机译：早期寿命增长模式持续12年，并影响囊性纤维化中的肺部结果
- 作者：Sanders Don B.;Zhang Zhumin;Farrell Philip M.;Lai HuiChuan J.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Growth;
- Growth faltering;
- Catch-up growth;
- Pulmonary function;
- Quantitative chest radiography;
- Lung disease;
89.Multicentre standardisation of chest MRI as radiation-free outcome measure of lung disease in young children with cystic fibrosis

机译：胸部MRI的多期标准化作为囊性纤维化患儿肺病的无源性结果测量
- 作者：Wielpuetz Mark O.;von Stackelberg Oyunbileg;Stahl Mirjam;Jobst Bertram J.;Eichinger Monika;Puderbach Michael U.;Naehrlich Lutz;Barth Sandra;Schneider Christian;Kopp Matthias V;Ricklefs Isabell;Buchholz Michael;Tuemmler Burkhard;Dopfer Christian;Vogel-Claussen Jens;Kauczor Hans-Ulrich;Mall Marcus A.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Magnetic resonance imaging;
- Functional lung imaging;
- Lung perfusion;
- Airway disease;
90.End-of-life practice patterns at US adult cystic fibrosis care centers: A national retrospective chart review

机译：美国成人囊性纤维化护理中心的寿命终身实践模式：国家回顾性图表审查
- 作者：Chen Elaine;Homa Karen;Goggin Jessica;Sabadosa Kathryn A.;Hempstead Sarah;Marshall Bruce C.;Faro Albert;Dellon Elisabeth P.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- End-of-life care;
- Hospice;
- Palliative care;
- Advance care planning;
- Lung transplant;
- Cystic fibrosis;
91.Poor recovery from a pulmonary exacerbation does not lead to accelerated FEV1 decline

机译：从肺癌的恢复不良不会导致加速FEV1下降
- 作者：Sanders Don B.;Li Zhanhai;Zhao Qianqian;Farrell Philip M.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Pulmonary exacerbation;
- FEV1;
- Epidemiology;
92.Prevalence and characteristics of chronic kidney disease among Danish adults with cystic fibrosis

机译：丹麦成年人患有囊性纤维化的慢性肾病的患病率与特征
- 作者：Berg Kristina H.;Ryom Lene;Faurholt-Jepsen Daniel;Pressler Tania;Katzenstein Terese L.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
93.Lung function decline is delayed but not decreased in patients with cystic fibrosis and the R117H gene mutation

机译：肺功能下降被延迟但囊性纤维化患者和R117H基因突变患者没有减少
- 作者：Wagener Jeffrey S.;Millar Stefanie J.;Mayer-Hamblett Nicole;Sawicki Gregory S.;McKone Edward F.;Goss Christopher H.;Konstan Michael W.;Morgan Wayne J.;Pasta David J.;Moss Richard B.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Cystic fibrosis;
- R117H;
- F508del;
- Lung function;
- Lung function decline;
94.Hypoglycaemia in patients with cystic fibrosis-harbinger of poor outcomes or innocent bystander?

机译：患有囊性纤维化患者的低血糖 - 差的成果或无辜的旁观者？
- 作者：Moheet Amir;Ode Katie Larson
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
95.Comparison of facemask and mouthpiece interfaces for multiple breath washout measurements

机译：用于多呼吸冲洗测量的面罩和吹嘴界面的比较
- 作者：Robinson Paul D.;Lum Sooky;Moore Courtney;Hardaker Kate M.;Benseler Nick;Aurora Paul;Cooper Peter;Fitzgerald Dominic;Jensen Renee;McDonald Reginald;Selvadurai Hiran;Ratjen Felix;Stanojevic Sanja
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Facemask;
- Lung clearance index;
- Functional residual capacity;
- Cystic fibrosis;
- Preschool;
96.No easy road to better cystic fibrosis care in Eastern Europe?

机译：在东欧更好的囊性纤维化护理没有简单的道路？
- 作者：De Boeck Kris;Fajac Isabelle
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
97.Cystic fibrosis patient registries: A valuable source for clinical research

机译：囊性纤维化患者注册表：临床研究的宝贵来源
- 作者：Dasenbrook Elliott C.;Sawicki Gregory S.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Cystic fibrosis;
- Patient registry;
98.The expression of Mirc1/Mir17-92 cluster in sputum samples correlates with pulmonary exacerbations in cystic fibrosis patients

机译：痰液中MiRC1 / miR17-92簇的表达与囊性纤维化患者的肺部加剧相关
- 作者：Krause Kathrin;Kopp Benjamin T.;Tazi Mia F.;Caution Kyle;Hamilton Kaitlin;Badr Asmaa;Shrestha Chandra;Tumin Dmitry;Hayes Don Jr.;Robledo-Avila Frank;Hall-Stoodley Luanne;Klamer Brett G.;Zhang Xiaoli;Partida-Sanchez Santiago;Parinandi Narasimham L.;Kirkby Stephen E.;Dakhlallah Duaa;McCoy Karen S.;Cormet-Boyaka Estelle;Amer Amal O.
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Cystic fibrosis;
- MicroRNA;
- Mir17-92a;
- Biomarker;
- Correlation;
- Pulmonary exacerbation;
99.Chronic infection sustained by a Pseudomonas aeruginosa High-Risk clone producing the VIM-1 metallo-beta-lactamase in a cystic fibrosis patient after lung transplantation

机译：在肺移植后，铜绿假单胞菌铜绿假单胞菌的慢性感染在囊性纤维化患者中产生Vim-1金属β-内酰胺酶
- 作者：Pollini Simona;Mugnaioli Claudia;Dolce Daniela;Campana Silvia;Neri Anna Silvia;Taccetti Giovanni;Rossolini Gian Maria
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期
- Chronic infection;
- Lung transplantation;
- Pseudomonas aeruginosa;
- ST235;
- Multidrug resistance;
- Carbapenemase;
100.Molecular characterization of gene regulatory networks in primary human tracheal and bronchial epithelial cells

机译：原发性人体气管和支气管上皮细胞基因调控网络的分子表征
- 作者：Gillen Austin E.;Yang Rui;Cotton Calvin U.;Perez Aura;Randell Scott H.;Leir Shih-Hsing;Harris Ann
- 期刊名称：《Journal of cystic fibrosis: official journal of the European Cystic Fibrosis Society》 | 2018年第4期

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