Ruptured Thoracoabdominal Aneurysm with Aortocaval Fistula, Aortic Dissection Type III, and Bilateral Femoral Aneurysms in Patient with Marfan Syndrome

摘要

According to our previous experience we decided to make transaortic suture, and preoperative diagnosis of fistula is a factor that increases survival rate.3 The feasibility of endovascular repair in Marfan syndrome is widely debated, because of potential risk induced by radial forces of the stent-graft upon the fragile aortic wall.4 Increase of aortic diameter of 15 mm/year followed by chest back pain on one side, general condition, and previous operations on the other were reasons to treat this patient by endograft implantation. [...] importance of surveillance of the patients with Marfan syndrome is well known, but one should not forget that they are at risk of gaining any cardiovascular complication, not just the most frequent ones, aortic root dilatation and dissection.