Müllerian anomalies occur in 0.1–0.5% of women [1].Failure of the paired müllerian ducts to fuse laterally canresult in uterus didelphys with obstructed unilateral vagina. This congenital disorder is often associated withrenal anomalies, such as ipsilateral renal agenesis, renaldysplasia, a double collecting system, and an ectopicureter [2–4]. Affected girls may present with low abdominal pain, severe dysmenorrhea, a pelvic or vaginalmass, abnormal vaginal discharge, and intermenstrualbleeding. These symptoms usually appear in adolescentgirls after menarche.
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