卡塔格内综合征一例报道并文献复习

摘要

卡塔格内综合征（KS）是临床罕见疾病，具有内脏转位、支气管扩张和慢性鼻窦炎三联征，早期正确诊断对 KS 患者的预后至关重要。本文报道1例被诊断为支气管扩张15年的 KS 患者，并结合以往文献对 KS 的临床特点、发病机制、治疗及预后进行总结，以加强临床对 KS 的认识。%Kartagener's syndrome(KS)is rare on clinic,mainly performed as triad signs including situs inversus, bronchiectasia and chronic nasosinusitis,early definite diagnosis is important to the prognosis. This paper reported a KS patient that diagnosed as bronchiectasia for 15 years,and reviewed the related literatures to summarize its clinical characteristics, pathogenesis,treatment and prognosis,to improve the awareness of clinicians.