婴儿胆汁淤积性肝病的营养治疗

摘要

There are various causes of cholestatic liver disease in infants that include extrahepatic biliary tract diseases, liver diseases, anatomical abnormality, metabolic or endocrine diseases, poisoning, infection, and so on. The causes leads to re-duction or interruption in bile lfow and thus results in nutrients malabsorption and comprehensive metabolic disorder. The aims of nutritional therapy for cholestatic liver disease are to reduce the risk of cholestasis related complications, to promote recov-ery of liver diseases, to restore bile flow, to promote growth and improve the comprehensive metabolic disorders, to improve quality of life and to prepare children for liver transplantation.%婴儿胆汁淤积性肝病的病因甚多，包括肝外胆道疾病、肝内疾病、解剖异常、代谢或内分泌疾病、中毒、感染等。由于胆流减少或中断，引起肠道营养物质吸收障碍及综合代谢紊乱。胆汁淤积性肝病的营养治疗，主要是减少胆汁淤积相关并发症；促进肝脏病变恢复，恢复胆流；促进生长发育和改善综合代谢紊乱；提高生存质量，为患儿后期肝移植奠定基础。